Abstract
Camptodactyly-arthropathy-coxa vara-pericarditis (CACP) syndrome is a rare disorder.
Patients with this syndrome experience early symptomatic arthropathy of the hips.
We report a case of adolescent siblings with bilateral arthropathy associated with
CACP syndrome in which total hip arthroplasty was performed as treatment of severe
associated disability. Postoperative Harris Hip Scores for patient 1 were 86 for the
right at 18 months and 96 for the left at 12 months. Postoperative Harris Hip Score
at 6 months for patient 2 was 53; however, he had good range of motion and lacked
deformity. Based on our limited experience and the limited available clinical data,
we feel that total hip arthroplasty is a reasonable treatment option for adolescents
with debilitating hip arthropathy associated with CACP syndrome.
Keywords
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Article info
Publication history
Published online: March 05, 2012
Accepted:
January 12,
2012
Received:
July 29,
2011
Footnotes
The Conflict of Interest statement associated with this article can be found at doi:10.1016/j.arth.2012.01.007.
Identification
Copyright
© 2012 Published by Elsevier Inc.
